ABSTRACT
Dentinogenesis Imperfecta is an autosomal dominant disorder of tooth development characterized by the presence of opalescent dentin, resulting in a dusky blue to brownish discoloration of the teeth. This condition is genetically and clinically heterogeneous, it may affect only the teeth or it may be associated with the Osteogenesis Imperfecta. It is inherited as autosomal dominant trait and in fact it is one of the most common dominantly inherited disorder in humans. The scalloping at the dentinoenamel junction is thought to help by mechanically interlocking the two hard tissues together. This locking is defective in these conditions which lead to enamel fracture easily from the defective dentin. The exposed dentin may then undergo severe and rapid attrition. Early diagnosis and proper treatment is mandatory in these conditions. Delay in the treatment can cause partial or complete loss of clinical crowns with healthy roots. A case report is discussed in which a young patient with Dentinogenesis Imperfecta was treated with maxillary fixed partial dentures and mandibular fibre reinforced overdentures with metal occlusal surfaces.